Misdiagnosing Bronchiectasis and Lymphangioleiomyomatosis

نویسندگان

  • Malihe Ghadir
  • Katayoon Najafizadeh
چکیده

This report presents a 25 year old female with a history of exertional dyspnea since the age of three. She was wrongly diagnosed and managed as bronchiectasis although she had had no productive cough or recurrent infection. At the age of 23, because of her dyspnea she was referred to a pneumologist for the first time. High resolution computed tomography and open lung biopsy was performed at that time. High resolution computed tomography showed diffuse thin walled cysts and pathologic results also confirmed lymphangioleiomyomatosis as her definite diagnose. She was treated with sirolimus and progesterone for two years which resulted in significant increase in oxygen saturation. However, no change was seen in forced expiratory volume at first second. *Corresponding author: Ghadir Malihe, NRITLD, Lung Transplantation Research Center, NRITLD, Masih Daneshvari Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran, E-mail: [email protected] Received January 04, 2013; Accepted February 25, 2013; Published February 28, 2013 Citation: Ghadir M, Najafizadeh K (2013) Misdiagnosing Bronchiectasis and Lymphangioleiomyomatosis. J Pulmon Resp Med 3: 139. doi:10.4172/2161105X.1000139 Copyright: © 2013 Ghadir M, et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.

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تاریخ انتشار 2013